The rigid spines in AS are susceptible to fractures, and the cervical spine is a major site of those injuries; furthermore, the rate of neurological involvement is high [
1,
4,
7,
8]. Although definite guidelines have not yet been established for the best treatment option of such fractures, reports of surgical treatment have increased while devices used in treatment have improved [
3,
4,
8]. Posterior longer internal fixation with a bone graft has become mainstream using a lateral mass screw or pedicle screw system; if necessary, some surgeons also prefer concomitant anterior plating. In the current case, a fracture line ran obliquely from the anterior C3-4 level to the posterior C4-5 level and was associated with great instability. Long and rigid internal fixation was essential due to the marked osteoporosis induced by both AS and aging; however, only C2 and C3 seemed to be usable anchors on the proximal side for fixation. Additionally, the patient's small physique and relatively small bones made screw insertion difficult at the upper cervical level. Therefore, we designed a long fusion from the occipit to the upper thoracic level to achieve a rigid internal fixation. On one hand, more rigid fixation would be expected extending fixation-end to the occipit, but on the other, there is a drawback of obliterating the mobile segment at the craniovertebral junction. Additional unintended surgery seemed to be difficult in this patient when loosening or dislodgement of screws occurred, and we chose the long fusion from occipit to upper thoracic spine. The RRS Loop Spine System developed by Shimizu et al. [
5] (
Fig. 6) is an instrumentation device for occipitocervical or occipit-upper thoracic fixation and has a unique occipit screw that has a design inspired by the screw used to bind a snow ski to its binding. This occipit screw enables secure fixation monocortically between the occipit bone and device. The rod, 4.76 mm in diameter, also contributes to rigid fixation of the spinal column. In the literature, the diagnoses of patients treated with this system have been mainly rheumatoid arthritis-related disorders or unstable anomalies of the craniocervical junction [
5,
6,
9]. This system could provide the solution for hyperextension injuries of the cervical spine, especially in the upper cervical region. Using the occipit as an anchor, stable fixation could be accomplished even in the case of an elderly patient or complex high-energy fracture with great instability [
10]. The connection between rod and vertebra is via a pedicle screw, hook, or sublaminar wiring in a similar manner to other instrumentation devices. We selected sublaminar banding by polyethylene tape and hook placement at the lower end lamina so that the stress caused by the instrumentation would be dispersed evenly through the occipit to the upper thoracic spine in this markedly osteoporotic patient. Our procedure seems to be one of the surgical methods that can successfully stabilize the spinal column depending on the fracture site despite the disadvantage of fixation to the occipit bone.